CT肺窗,示双肺磨玻璃样阴影,主要累及上叶或肺门周围.Monia)分为:特发性肺纤维化(idiopathic pulmonary fibrosis,IPF,即普通型间质性肺炎,usual interstitia pneumonia,UIP)、非特异性间质性肺炎(nonspecific interstitial pneumonia,NSIP)、隐源性机化性肺炎(cryptogenic organizing pneumonitis。特发性间质性肺炎、慢性支气管炎和胶原病等所致肺纤维化的临床表现缺少特异性,CT ......