特发性间质性肺炎(idiopathic interstitial pneumonias,IIP)系指原因不明、以弥漫性肺间质病变为主要特征的一组肺疾病。主要包括:①普通型间质性肺炎(usual interstitial pneumonia,UIP)。隐源性机化性肺炎(cryptogenic organizing pneumonia, COP),即特发性闭塞性细支气管炎机化性肺炎(idiopathic bronchiolitis obliterans with organizing pneumonia,IB ......