慢性进行性眼外肌麻痹(chronic progressive ex‐ternal ophthalmoplegia,CPEO)或称为von Graefe‐Fuchs眼肌病(ocularmyopathy of von Graefe‐Fuchs),是主要累及并局限于眼外肌的慢性进行性肌病。常见于Kearns‐Sayre综合征(Kearns‐Sayre syndrome,KSS)。近年来研究证实,CPEO实际上是一种线粒体脑肌病(mitochondrial encephalomyopathy)(见第十六章神经系统 ......