肺朗格汉斯细胞组织细胞增生症(pulmonary Langerhans cell histiocytosis,PLCH)亦称肺组织细胞增生症X(pulmonary histiocytosisX。PHX)、肺朗格汉斯细胞肉芽肿病(pulmonary Langerhans cell granulomatosis)或肺嗜酸性肉芽肿(pulmonary eosino‐philic granuloma)[ 244,245 ],它是一种目前原因不清的肺间质病变,其特点是Langerhans细胞瘤性增生[ 246 ]。 ......