先天性肾囊性疾病( congenital renal cystic diseases )多与遗传性疾病有关,共同形态特点是双侧肾不同水平的多囊性改变,包括多囊肾( polycystic kidney ) ,海绵肾( medullary sponge kidney ) ,肾髓质囊性病( medullary cystic disease of disease ) 。多房性囊性肾发育不良( multi-cystic dysplastic kidney )等。按遗传方式可分为婴儿型多囊肾与成人型多囊肾(表7 - ......