长链酰基辅酶A脱氢酶( LCHAD )缺陷症主要包括长链酰基辅酶A脱氢酶缺陷症、长链L-3 -羟酰基辅酶A脱氢酶( long-chain L-3 - hydroxyacyl-CoA dehydrogenase , LCHAD )缺陷症、中链酰基辅酶A脱氢酶( medium-chain acyl-CoA dehydrogenase deficiency 。MCAD )缺陷症和短链酰基辅酶A脱氢酶( short-chain acyl-CoA dehydrogenase deficiency , SCAD )缺 ......