嗜血细胞综合征(hemophagocytic syndrome)是一组以发热、肝脾肿大、出血、全血细胞减少为特征的临床综合征。由感染诱发者称为感染相关嗜血细胞综合征(infection‐as‐sociated hemophagocytic syndro me,I A HS或V A HS),由恶性肿瘤诱发者称为恶性肿瘤相关嗜血细胞综合征(malignency‐associated hemophagocytic syndro me,MA HS)。二者均属继发性嗜血细胞淋巴组织细胞增生症(secondary h ......