肾的囊性畸形(cystic malfor mation of kidney)多与遗传性疾病有关,共同形态特点是双侧肾脏不同水平的多囊性改变,包括多囊肾(polycystic kidney),髓质海绵肾(medullary sponge idney),肾髓质囊性病(medullary cystic disease)。D ﹒沿输尿管长轴矢状曲面MPR,示输尿管向前下跨过融合的肾下极下行(箭头). ......