病变在下丘脑-神经垂体者称为中枢性尿崩症( central diabetes insipidus , CDI ) 。由AVP-NPII基因突变所致的尿崩症称为家族性常染色体显性遗传性神经垂体性尿崩症( autosomal dominant form of familial neurohypophyseal diabetes insipidus , adFNDI )或常染色体显性遗传神经垂体性尿崩症( autosomal dominant neurohypophyseal diabetes insipidu ......