参考文献：迅速的认知功能下降

Mr imaging of familial creutzfeldtjakob disease : a blinded and controlled study .A novel human disease with abnormal prion protein sensitive to protease .Phenotypic heterogeneity and genetic modification of p102l inherited prion disease in an international series .Clinical presentation and pre-mortem diagnosis of variant creutzfeldt-jakob disease associated with blood transfusion : A case report .Diagnosing variant creutzfeldt-jakob disease with the pulvinar sign : Mr imaging findings in 86 neuropathologically confirmed cases .